2. Developmental Dysplasia Of The Hip (DDH)
• includes a wide spectrum of hip alterations:
• Neonatal instability;
• acetabular dysplasia;
• hip subluxation;
• true dislocation of the hip
3. • Syndromic types:
• DDH can be a part of many or only a sole manifestation of skeletal dysplasia,
or it may be present in conjunction with other malformations, e.g., pes -
equinovarus and acetabular labrum abnormalities.
• Syndromic dysplasia exists also in association with different pathologies such
as Down’s syndrome and neurogenic, renal or cardiovascular abnormalities.
• Non-syndromic DDH:
• diagnosed as an isolated condition
• genetic component
• These are mainly variants of genes whose products are structural factors of
connective tissue, genes involved in osteo- and chondrogenesis, genes
associated with the formation of joint structure and chemokine reseptors
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20. •In older infant or child,
• Barlow and Ortolani examination is of limited utility due to
the development of contractures.
• These patients are observed for:
• leg length discrepancy, thigh-fold asymmetry, and limited hip
abduction.
• Leg length discrepancy should be assessed for with the infant in
the supine position with the pelvis flat on a level surface and the
hips and knees flexed to 90°. A discrepancy is indicated by
unequal knee heights, which is termed the Galeazzi sign
• in a child >3 months old is an assessment for asymmetric
diminished hip abduction
21.
22. • The walking child may also present with:
• a Trendelenburg gait (trunk tilt toward the affected hip
when weight is applied) if there is a unilateral dislocation
• a waddling gait (trunk tilt toward the weight-bearing side,
alternating throughout the gait cycle) if there is bilateral
dislocation
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37. Ultrasonography
• allows for the visualization of the femoral head location relative to the
acetabulum and specific anatomic parameters, such as the depth of
the acetabulum and inclination of the acetabular roof.
• can be performed in a static or dynamic manner:
• static study: examine the joint anatomy (the shapes and relations between
the femoral head, acetabulum, and labrum).
• dynamic ultrasonography, hip joint stability is assessed by performing the
manipulative stress maneuvers under direct imaging observation
38. • Key ultrasound measurements include
• the α (which is formed by the bony ilium and the bony roof of the
acetabulum)
• Values >60 degrees are considered normal, and those <60degree imply
acetabular dysplasia
• the β angle (which is formed by the bony ilium and the labral
fibrocartilage),
• Normal value <50degree, as the femoral head subluxates, the beta angle
increase
• the percentage of the femoral head covered by the bony roof of
the acetabulum.
• The α angle has more clinical significance than the β angle
39.
40. Treatment
• the goal of the treatment is to achieve a concentric reduction of the
femoral head into the acetabulum and correct development of all
structures of the hip.
• This can be achieved according to three main principles:
• To achieve a concentric and stable reduction of the hip, avoiding
complications such an AVN.
• To confirm correction of acetabular dysplasia due to the stimulus provoked by
the stable and concentric position of the femoral head into the acetabulum.
• Pelvic or femoral osteotomies are indicated in two situations.
• First, when there is a residual dysplasia that previous reduction of the hip has not been
able to correct.
• Second, when the potential of correction after hip reduction is expected to be not
enough to correct the acetabular dysplasia due to the child’s age.
41.
42. Pavlik Harness
• used for all degrees of hip
dysplasia in otherwise normal
newborns.
• Evolved as the clear method of
choice for treatment of infants
with developmental hip dysplasia
or dislocation
• Use of the Pavlik harness is
contraindicated:
• when there is major muscle
imbalance, as in myelomeningocele
(L2 to L4 functional level)
• major stiffness as in arthrogryposis;
• Ligamentous laxity, as in Ehlers-
Danlos syndrome.
43. 4 steps for application of the Pavlik harness
1. The chest halter is applied.
• The shoulder straps on the halter should
cross in the back to prevent them from
sliding over and down the child’s shoulders.
2. The leg stirrup straps are applied. The
strap for the proximal part of the leg
should be located just distal to the
popliteal fossa.
• This strap stabilizes and controls the knee
and, when properly positioned, prevents
bowstringing of the anterior and posterior
stirrup straps.
• With bowstringing, tightening of the
posterior stirrup straps often produces
internal rotation and adduction of the hip.
44. 3. The anterior stirrup straps are
attached to the chest halter.
• The attachment for the anterior
(flexor) stirrup straps should be
located at the anterior axillary line.
• If these straps are placed too far
medially, tightening them will cause
not only flexion but also adduction
of the hip.
4. Lastly, the posterior (abduction)
stirrup straps should be
attached over the scapula.
• The position should be set to hold
the hip in 90° of flexion with the
posterior straps limiting adduction
to prevent dislocation.
45. Treatment of the Infant with Acetabular
Dysplasia with or without Hip Subluxation
• Pavlik harness can be used for infants with limited hip abduction
and documented acetabular dysplasia with or without subluxation
• the infant with dysplasia should be removed from the harness daily
for baths and should be worn for 23 hours daily until the findings of
clinical and radiographic examination are normal
46. • To achieve this goal, the harness must
be worn :
• minimum of three months by children
<3mo old
• approximately double their age for children
>4mo old
• part-time during the last two months
• child approaches the walking age, an
alternative form of bracing such as a plastic
hip abduction brace
47.
48.
49. Abduction Orthosis
• Should be considered as an alternative to the Pavlik harness for
infants more than nine months of age who require continued
abduction positioning because of acetabular dysplasia and/or
subluxation.
• This device maintains abduction while allowing walking, and it is more
acceptable for the larger child.
• An abduction orthosis can be used for patients up to two and one-
half years of age.
• After about eighteen months of age, it is usually used only at night,
depending on the radiographic appearance of the hip.
50. Skin Traction Followed by Closed Reduction
• is the recommended treatment for older infants months of
age with a dislocated hip for which attempted reduction
with the Pavlik harness has failed or for children over nine
.
• This sequence of treatment decreases muscular
contractures and allows a safer, gentle closed reduction.
51. • After two to three weeks of skin
traction, an adductor tenotomy
is performed with the child
under general anesthesia, closed
reduction is attempted,
arthrography is performed
through a medial approach, and
a spica cast is applied.
• The cast is applied with the hip
held in 100° of flexion and 40° to
50° of abduction the so-called
human position
52. • The overall goals in the management of infants with developmental
dislocation of the hip are
• early diagnosis,
• safe and effective reduction of the hip,
• minimal inconvenience for the child and family,
• decreased cost by avoiding prolonged hospitalization,
• decreased risks by avoiding anesthesia and spica casts.
• The results indicate that these goals can best be achieved by
understanding Pavlik’s method (the correct use of his harness) and
using ultrasonography to aid in diagnosis and management.
53. Operative Treatment of Developmental Hip
Dislocation
• required for children between the ages of six and eighteen months
when treatment with a Pavlik harness and/or closed reduction
attempts have failed.
• The decision to perform an open reduction must be made in the
operating room following arthrography and failed closed reduction.
54. Anteromedial Open Reduction (in Children Six
to Twenty-four Months of Age)
• Clear anteromedial exposure allows:
• lengthening of the psoas tendon and
• opening of the constricted capsule, especially the capsule with an hourglass
constriction seen in most dislocated hips and
• released of the constricted transverse acetabular ligament at the acetabular base.
• The femoral head can then be safely reduced.
• stability is provided by application of the spica cast with the child in the
“human position”
• Problems with the anteromedial open reduction include:
• Capsulography cannot be performed
• redislocation (even in the spica cast),
• late avascular necrosis,
• and residual dysplasia.
55. Anterior Open Reduction Surgical Approach to
the Older Child (Two Years of Age and Older)
• This technique avoids the need for prolonged preliminary
traction and has proved to be as effective in younger children
as it is in three to four-year-old children
• single-stage approach to reduction in the older child, which
includes ;
• capsulorrhaphy,
• femoral derotational shortening,
• acetabuloplasty.
56. Open Reduction, Including Femoral Shortening
and Acetabuloplasty
• The goal of a one-stage reduction is :
• to safely reduce the dislocated hip and
• to surgically recreate normal anatomy (as closely as possible) that will
maintain the reduction
• allow rapid development of normal hip function.
• The patient is placed on a radiolucent operating table in a supine (but
30° oblique) position with a sandbag under the chest but not under
the hip as that prevents good skin preparation and good image-
intensifier views.
61. Acetabuloplasty
• perform this procedure in all patients treated with primary open
reduction and femoral shortening
• Salter procedure is that it redirects the acetabulum, thus immediately
improving anterolateral coverage of the femoral head
• With other types of acetabuloplasty(especially the Pemberton
acetabuloplasty),there is some risk of decreasing acetabular size
because the technique includes bending through the triradiate
cartilage
62. Cast Immobilization
• After the single-stage hip reduction is complete, suction drainage
tubes are placed in each wound and the wounds are closed, ending
with a cosmetic subcuticular suture.
• The child is placed in a hip spica cast with the hip flexed and abducted
30°
• The hip spica cast is maintained for six weeks and then is changed (as
a day-surgery procedure with the patient under general anesthesia)
to a second, more loosely fitting hip spica cast, which is worn for
another four to six weeks.
63. • A Petrie cast can be used for the second cast; however, in young
children (especially those who are overweight), such a cast produces
excessive stress at the osteotomy site.
• Therefore, a loosely fitting second hip spica cast is preferred. The
second cast is removed ten weeks after surgery, and no subsequent
bracing is required in the typical case.
64. Reference
• Developmental Hip Dysplasia and Dislocation: Part II,Stuart L.
Weinstein, Scott J. Mubarak and Dennis R. Wenger, J Bone Joint Surg
Am. 2003;85:2024-2035.
• Developmental Hip Dysplasia and Dislocation: Part II,Stuart L.
Weinstein, Scott J. Mubarak and Dennis R. Wenger, J Bone Joint Surg
Am. 2003;85:1824-1832.
• Developmental Dysplasia of the Hip :Scott Yang, a Natalie Zusman,, a
Elizabeth Lieberman, a Rachel Y. Goldstein, PEDIATRICS Volume 143,
number 1, January 2019
• Developmental dysplasia of the hip: update of management:EFORT
Open Rev 2019;4:548-556.
• Developmental Dysplasia of the Hip: A Review of Etiopathogenesis,
Risk Factors, and Genetic Aspects Stefan Harsanyi , Radoslav
Zamborsky, Lubica Krajciova, Milan Kokavec,Lubos Danisovic:Medicina
2020, 56, 153; doi:10.3390/medicina56040153
Notes de l'éditeur
Looseness or laxity within the acetabulum is called instability
In the case of dysplasia, some morphological changes in the acetabulum, proximal femur or both are present, but articular surfaces are concentrically in contact
In the subluxated hip, there is contact between both articular surfaces, but not concentrically
In a true dislocation, there is no contact between the articular surfaces of the proximal femur and acetabulum.
laxity of the femoral head is present after birth, Neonatal Hip Instability (NHI) can be diagnosed and present for the first few weeks of life, has a mild course and up to
88% of cases of NHIs have a spontaneous resolution by the eighth week of life
Can appear at newborn or later
Problem arrive from socket/acetabulum or femoral head
The hip joint begins to develop physiologically from mesenchymal cells as early as the fifth or sixth gestational week.
By the eleventh week, the femoral head is completely formed [8], and in the coming weeks it undergoes a more rapid growth than the acetabular cartilage, causing about 50% of the femoral cartilage to be present at the time of birth, but in the postnatal period, the cartilage begins to develop much faster.
Adequate growth and development of the hip depends on two main (and necessary) factors: concentric positioning of femoral head into the acetabular cavity and adequate balance in growth between triradiate and acetabular cartilage
Any alteration in these two conditions leads to a hip dysplasia
It seems that most of the changes that lead to a DDH appear in the last months of intrauterine life.
The Barlow maneuver is performed by adducting the hip to the midline and gently applying posterior force. A positive Barlow result is when the femoral head subluxes, and a clunk is felt. A Barlow-positive hip indicates that the femoral head is resting in the acetabulum but has pathologic instability.
With the thighs adducted and posteriorly depressed, the Ortolani maneuver is performed by abducting the hips while applying anterior-directed pressure at the greater trochanters. An Ortolani maneuver is considered to have a positive result if the femoral head relocates with a distinct clunk. An Ortolani-positive hip is more severe than a Barlow-positive hip because it indicates that the femoral head is dislocated at rest.
The femoral head ossification nucleus is visible radiographically at ∼4 to 6 months of age.
Hence, radiographs are not recommended for DDH evaluations before 4 months of age. After ∼6 months of age, radiographs are the preferred method of evaluating and monitoring DDH after femoral head ossification more reliably appears.
H is drawn as a horizontal line, connecting the bilateral acetabular triradiate cartilage
Vertical line over the lateral edge of acetabular at the long axis of femur
Normal hip at lower medial quadrant
Dislocate: upper lateral quadrant
Aacetabular index:
Angle between horizontal line of hilgenreiner and the line between the two edge of the acetabulum
Normal hip 20-30
Dislocate or dysplastic hip >30
Pelvic osteotomies are performed after the age of three to four years, when the acetabular potential of correction diminishes
Patient follow up every week
At that time check the stability of the hip
PH discontinue 6week after clinically hip stable is obtained
To weaning of up to 2hrs per week until brace is worn at night time
It is recommended that a newborn with a true dislocation wear the harness full-time for several weeks until the dislocatable hip has stabilized in the acetabulum
The hip spica cast in the human position (used with the Ludloff approach) ideally centers the hip for acetabular growth but has associated risks, including that of an increased rate of avascular necrosis33. This form of avascular necrosis is usually mild and may
be due to posterolateral labral pressure on the delicate vessels that ascend the femoral neck.
Also, this position of hip hyperflexion is maintained for three to four months, and the required transition to full hip extension for walking
(after cast removal) may stress the capsule and may be a cause of residual dysplasia.
For these reasons, most pediatric orthopaedic surgeons use the anteromedial approach primarily in children younger than one year of age
Anterolateral (Salter) incision and a separate lateral longitudinal incision over the femur for the femoral shortening. With femoral shortening, an adductor tenotomy is unnecessary because tension is reduced n all muscle groups, including the adductors.
Diagrams illustrating the technique for anterior exposure of a dislocated hip.
A: The abductor muscles are stripped from the lateral wing of the ilium, and a space above the hip capsule is developed.
B: With further retraction and dissection, a complete capsular exposure is performed. This includes exposing the anterosuperior and posterior portions of the capsule.
Diagram demonstrating the Salter-type capsulorrhaphy.
A: outline of the planned cut in the anterior and superior capsular
area.
B: Excision of the superolateral and posterior segment of redundant capsule (gray shaded area).
C: Internal rotation of the capsule after the hip has been reduced. Point A, which was on the anterior aspect of the neck, is now rotated to point A′, which represents a point just distal to the anterior inferior iliac spine. The inferior capsular flap (B) is rotated medially and sutured to the periosteum of the pubis (B′).
D: After careful suturing with nonabsorbable sutures. This suturing has the quality of a hernia repair.
A method for planning the derotational shortening femoral osteotomy. Smooth pins are placed in
the greater trochanteric area and in the distal femoral condyles at an angle equal to the planned
degree of anteversion correction. After derotation, the pins are parallel in the transverse plane.
The femoral shortening osteotomy is then performed with removal of a 1.5 to 2.5-cm segment, as determined by the amount of overlap
Present with the hip reduced. The osteotomy site is fixed with an appropriately sized blade-plate.
In such cases, the four-hole AO mandibular plate is placed anteriorly, bridging the shortening osteotomy at the intertrochanteric level. This plate allows dynamic compression and secure fixation
Sequence of the derotational femoral shortening osteotomy.
A: A subtrochanteric cut is made after the guide-pin and AO chisel have been inserted properly.
B: Overlap method to determine the amount to shorten the femur. The femoral head is reduced in the socket for this assessment.
C: Internal fixation with an appropriate blade-plate.